SYSTEM FINDING ASSOCIATED ILLNESSHypoactive reflexes Familial dysautonomiaJoint tenderness Familial Mediterranean fever, rat-bite fever, systemic lupus erythematosus, Lymedisease, lymphogranuloma venereum, brucellosis,hyperimmunoglobulinemia D syndrome, tumor necrosis factor receptorassociatedperiodic syndromeMuscle tenderness Brucellosis, trichinellosis, arboviral infection, dermatomyositis, polyarteritis,subdiaphragmatic abscess (trapezius tenderness)Spinal tenderness Subacute vertebral osteomyelitis, infective endocarditis, brucellosis,typhoid feverOropharynxAnomalous dentition Anhidrotic ectodermal dysplasiaDental or fascial abscess Sinusitis, brain abscess, mediastinal abscessEpistaxis Relapsing fever, leukemia, psittacosis, rheumatic feverGingival hypertrophy Leukemia, Langerhans cell histiocytosisPharyngeal hyperemia Cytomegalovirus, Epstein-Barr virus, toxoplasmosis, tularemia, leptospirosisSmooth tongue Familial dysautonomiaUlcerations Behçet disease; periodic fever, aphthous stomatitis, pharyngitis, and adenitis(PFAPA); hyperimmunoglobulin D syndromeSkin (limited review)Blotchy skin Familial dysautonomiaDecreased body hair, hypohidrosis Anhidrotic ectodermal dysplasiaDehydration Diabetes insipidus, ectodermal dysplasia, familial dysautonomiaErythema nodosum Infection, juvenile idiopathic arthritis, systemic lupus erythematosus,malignancy, inflammatory bowel diseaseErythema migrans Lyme disease, southern tick-associated rash illness (STARI)Eschar TularemiaMacular salmon-pink rash Juvenile idiopathic arthritisMalar erythema Systemic lupus erythematosusPalpable purpuric lesions Polyarteritis nodosaPetechiae Endocarditis, bacteremia, viral infection, rickettsiaSeborrheic rash HistiocytosisUrticarial macular rash Serum sickness, familial cold autoinflammatory syndrome, Muckle-Wellssyndrome, neonatal-onset multisystem inflammatory disease
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